Updated on 2 August 2012
India performs first-of-its-kind cardiac surgery in world
Bangalore: Chennai-based MIOT Hospitals successful performed a surgery on a 14-year-old boy from Mumbai, who was suffering from several disorders including the breast bone pushing the whole heart to left side of the chest thereby compressing the lungs, a hole in the heart, a bulge in the heart's biggest blood vessel and a leaky valve.
All these disorders are features of Noonan's syndrome, which is an autosomal congenital disorder considered to be a type of dwarfism. The typical features of this syndrome also include, webbed neck and a flat nasal bridge. It occurs one-in-1,000 child births.
The boy was diagnosed to have a large hole in the heart (ASD) as a child at the age of four and was also suffering from progressive breathlessness. He was further diagnosed to have a large aneurysm of the aorta with a leak in the aortic valve, while he underwent treatment for the hole in the heart.
This combination of aneurysm of the aorta with leak in the aortic valve and a hole in the heart has not been reported before. The young boy in addition had a chest wall abnormality called pectus excavatum in which the breast bone has gone very deep and this has pushed the heart completely to the left side of the chest.
The boy was referred to MIOT Hospitals for surgery after he was having breathlessness and was unable to sleep properly. Normally, open heart surgery is performed by cutting the breast bone because the heart is pushed behind. Done this way, the operation is easy to perform. However, in case of this young boy, since the heart was totally on the left side of the chest, it was impossible to do this operation through the midline. There is not a single case report of this combination of disease in the world.